Table 2. Clinical Evaluation for Elevated AST/ALT and Time to Diagnosis of Muscle Disease
Liver ImagingLiver BiopsyTime to CK Measurement (months)Time to Neurology Consultation (months)Time to Diagnosis (months)
USNo3.51617
USNo0.531
USNo244
NoneNo22Undiagnosed
USNo123
MRI, MRCP, HIDALaparoscopic biopsy9911
NoneNo0.7512.5
USNeedle biopsy141415
MRI, MRVNeedle biopsy151618
USLaparoscopic biopsy242531
USNo45.54
USNo810Undiagnosed
N/AN/A7.0 (average)9.0 (average)10.7 (average)
  • AST/ALT, aspartate aminotransferase/alanine aminotransferase; HIDA, Hepatobiliary Iminodiacetic acid scan; MRCP, magnetic resonance cholangiopancreatography; MRI, magnetic resonance imaging; MRV, magnetic resonance venography; US, ultrasound.