Table 3.

Rare Causes of Leg Edema in the United States

UnilateralBilateral
Acute (<72 hours)ChronicAcute (<72 hours)Chronic
Primary lymphedema (congenital lymphedema, lymphedema praecox, lymphedema tarda)Primary lymphedema (congenital lymphedema, lymphedema praecox, lymphedema tarda)
Congenital venous malformationsProtein losing enteropathy, malnutrition, malabsorption
May-Thurner syndrome (iliac-vein compression syndrome)51Restrictive pericarditis
Restrictive cardiomyopathy
Beri Beri
Myxedema